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Genome-wide Meta-analysis finds the ACSL5-ZDHHC6 locus Is associated with ALS and links weight loss to the disease genetics
Journal article   Open access   Peer reviewed

Genome-wide Meta-analysis finds the ACSL5-ZDHHC6 locus Is associated with ALS and links weight loss to the disease genetics

A. Iacoangeli, T. Lin, A. Al Khleifat, A.R. Jones, S. Opie-Martin, J.R.I. Coleman, A. Shatunov, W. Sproviero, K.L. Williams, F. Garton, …
Cell Reports, Vol.33(4), Art. 108323
2020
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Abstract

We meta-analyze amyotrophic lateral sclerosis (ALS) genome-wide association study (GWAS) data of European and Chinese populations (84,694 individuals). We find an additional significant association between rs58854276 spanning ACSL5-ZDHHC6 with ALS (p = 8.3 × 10−9), with replication in an independent Australian cohort (1,502 individuals; p = 0.037). Moreover, B4GALNT1, G2E3-SCFD1, and TRIP11-ATXN3 are identified using a gene-based analysis. ACSL5 has been associated with rapid weight loss, as has another ALS-associated gene, GPX3. Weight loss is frequent in ALS patients and is associated with shorter survival. We investigate the effect of the ACSL5 and GPX3 single-nucleotide polymorphisms (SNPs), using longitudinal body composition and weight data of 77 patients and 77 controls. In patients’ fat-free mass, although not significant, we observe an effect in the expected direction (rs58854276: −2.1 ± 1.3 kg/A allele, p = 0.053; rs3828599: −1.0 ± 1.3 kg/A allele, p = 0.22). No effect was observed in controls. Our findings support the increasing interest in lipid metabolism in ALS and link the disease genetics to weight loss in patients.

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Collaboration types
Domestic collaboration
International collaboration
Citation topics
1 Clinical & Life Sciences
1.52 Neurodegenerative Diseases
1.52.765 ALS Mechanisms
Web Of Science research areas
Cell Biology
ESI research areas
Molecular Biology & Genetics
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